Monostotic fibrous dysplasia in the proximal tibial epiphysis: a case report

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• 作者：Ji-Yong Gwark (28)
  Jin-Hoon Jeong (28)
  Sun-Chul Hwang (28)
  Dae-Cheol Nam (28)
  Jeong-Hee Lee (29)
  Jae-Boem Na (30)
  Dong-Hee Kim (28)
  
  28. Department of Orthopaedic Surgery ; Research Institute of Clinical Medicine ; Gyeongsang National University School of Medicine and Hospital ; 15 Jinju-daero 816 beon-gil ; Jinju ; 660-750 ; South Korea
  29. Department of Pathology ; Gyeongsang National University School of Medicine and Hospital ; Jinju ; Korea
  30. Department of Radiology ; Gyeongsang National University School of Medicine and Hospital ; Jinju ; Korea
  
• 关键词：Bone tumor ; Epiphysis ; Fibrous dysplasia
• 刊名：Journal of Medical Case Reports
• 出版年：2014
• 出版时间：December 2014
• 年：2014
• 卷：8
• 期：1
• 全文大小：875 KB
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  3. McCune, DJ, Bruch, H (1937) Osteodystrophia fibrosa: report of a case in which the condition was combined with precocious puberty, pathologic pigmentation of the skin, and hyperthyroidism, with a review of the literature. Am J Dis Child 52: pp. 806-848 CrossRef
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• 刊物主题：Medicine/Public Health, general; General Practice / Family Medicine; Public Health; Primary Care Medicine;
• 出版者：BioMed Central
• ISSN：1752-1947

文摘

Introduction Fibrous dysplasia is one of many well-known disorders in which there is a defect in the remodeling process of immature bone to mature into lamellar bone, and it often exists in metaphyseal and diaphyseal parts of the long bone. In this report, we describe a rare case where fibrous dysplasia was found only in the proximal part of the epiphysis of the tibia without other bony lesions. Case presentation A 14-year-old Asian girl was referred to our hospital after slipping down with pain on the left knee. A radiograph showed an abnormal finding of a central radiolucent lesion with a marginal sclerotic border near the proximal tibial spine. A magnetic resonance image showed the lesion at low signal intensity on a T1-weighted image and at high signal intensity on a T2-weighted image. The biopsy results led us to conclude that the lesion was a fibrous dysplasia. Conclusion If an abnormal lesion on the epiphysis, especially in long bones, is detected on a radiograph, several differential diagnoses can be made. Although fibrous dysplasia is usually not encountered as an epiphyseal lesion, it is important to incorporate all the clinical, radiographic and pathologic features to diagnose monostotic fibrous dysplasia when the lesion is located at the epiphyseal location.