摘要
<正>Erdheim-Cheste病(ECD)是一种非常罕见的非朗格罕组织细胞增生症~[1]。发病机制目前不详,目前已知是一群CD68(+)、CD1a(-)、S-100(±)为特征的非朗格汉斯细胞在全身各个器官浸润所致,在这些患者首发症状为骨痛,多数患者伴有心血管、中枢神经系统、肾脏、乳腺受累~[2-3]。笔者于2015-03收Erdheim-
引文
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