Primary localized tracheobronchial amyloidosis presenting with massive hemoptysis: a case report and literature review
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- 作者：Li-qin Zhang ; Yi-chao Zhao ; Xiao-wei Wang ; Jian Yang ; Zhi-wei Lu and Yu-sheng Cheng
- 刊名：The Clinical Respiratory Journal
- 出版年：2017
- 出版时间：January 2017
- 年：2017
- 卷：11
- 期：1
- 页码：122-125
- 全文大小：310K
- ISSN：1752-699X
文摘
Primary localized tracheobronchial amyloidosis (TBA) is a rare respiratory tract dysfunction, which is a heterogeneous group of diseases involving abnormal extracellular deposition of amyloid and autologous fibrillar protein material in β-pleated sheets. A 64-year-old man was referred to our hospital because of hemoptysis. Physical examination showed decreased breath sounds in the right lung on auscultation. Chest computed tomography scan displayed multiple nodules with varied size in main bronchia around bilateral hilus of the lung. After admission, bronchoscopy was performed for this patient, and roughness of mucosa in trachea and multiple nodules in respiratory tract were observed. Through further tissue biopsy, the diagnosis of primary TBA was confirmed.