A rare case of accessory maxilla and bilateral Tessier no. 7 clefts, a 10-year follow-up

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• 作者：Ali Borzabadi-Farahani ; Stephen L.-K. Yen ; Cameron Francis ; Pedro A. Lara-Sanchez ; Jeffrey Hammoudeh
• 关键词：Maxillary duplication ; Accessory maxilla ; Bilateral Tessier no. 7 cleft ; Macrostomia
• 刊名：Journal of Cranio-Maxillofacial Surgery
• 出版年：2013
• 出版时间：September, 2013
• 年：2013
• 卷：41
• 期：6
• 页码：527-531
• 全文大小：1453 K

文摘

A Tessier no. 7 cleft is a lateral facial cleft which originates from the oral cavity and extends towards the tragus, involving both soft-tissue and skeletal components. A male patient presenting with both maxillary jaw duplication and bilateral Tessier no. 7 clefts, which has been reported only twice in the literature, is described. Bilateral facial clefts, macrostomia and chondro-cutaneous remnants were noted, which were repaired and resected. With further growth, facial asymmetry and asymmetric facial nerve dysfunction became apparent. Radiographic examination showed an accessory maxillary jaw and?a flattened and hypoplastic right coronoid process. A maxillary alveolar cleft was also present between the left second bicuspid and the second permanent molar. This case may represent an under-recognized phenotype with an unusual combination of maxillary jaw duplication, macrostomia, Tessier no. 7 clefts, and chondro-cutaneous remnants. A long-term follow-up of these patients is recommended as they often develop craniofacial deformities later in life.