The ages of the children were between 6 and 17 (mean age 11.9) and 32 (42.9 % ) of them were girls and 43 (57.1 % ) were boys. Three cases (4 % ) were diagnosed as AN in our study, however, no risk factors were determined in two of them. A history of hearing loss following a vaccination was found in only one patient.
Our data show that the incidence of AN in the children with severe hearing loss is not negligable. Therefore, our results suggest that automatic ABR should be also used with OAE as a routine application in the neonatal screening programmes, since the solely use of OAE in the neonatal screening programmes may result in the delay of the diagnosis of the children with AN.
Auditory neuropathy/auditory dys International Journal of Pediatric Otorhinolaryngology |
International Journal of Pediatric Otorhinolaryngology, Volume 70, Issue 7, July 2006, Pages 1299-1306 Raymond Y.S. Ngo, Henry K.K. Tan, A. Balakrishnan, Sok Bee Lim, Derek T. Lazaroo Abstract SummaryThe implementation of neonatal hearing screening has enabled early detection and intervention in hearing loss. The use of otoacoustic emissions (OAE) and auditory brainstem response testing in universal screening has led to the recognition of this recently described disorder called auditory neuropathy/auditory dys-synchrony (AN/AD). This diagnosis indicates that the infant has significant hearing loss despite having normal outer hair cells in the cochlea. We reviewed the characteristics and natural history of nine infants detected to have AN/AD from universal newborn hearing screening in a national pediatric hospital. Fifty-two cases of hearing loss were detected from 14,807 consecutively screened cases. Of the 52 cases, 9 had electrophysiological test results consistent with AN/AD. They include both premature infants who had major neonatal complications and term infants with no perinatal complications. Six cases had bilateral and three cases had unilateral findings. We suggest that AN/AD can occur in low-risk infants and hence screening of high-risk cases alone is insufficient. Our findings are discussed with reference to the current literature. |
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