Cardiac Malformations in Patients With Pentalogy of Cantrell and Ectopia Cordis

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• 作者：Jesú ; s de Rubens Figueroa^a ; ^{derubens@hotmail.com"" rel=""nofollow} ; Erika Flor Sosa Cruz^a ; Luisa D&#xed ; az Garc&#xed ; a^b ; Daniel Carrasco Daza^c
• 关键词：Congenital heart disease ; Ectopia cordis ; Pentalogy of Cantrell
• 刊名：Revista Española de Cardiología (English Edition)
• 出版年：2011
• 出版时间：July 2011
• 年：2011
• 卷：64
• 期：7
• 页码：615-618
• 全文大小：670 K

文摘

We studied 21 patients who presented with a diagnosis of pentalogy of Cantrell. Their mean age was 40 days. All patients presented with congenital heart disease. Six presented with ectopia cordis. Every patient was subjected to echocardiography. Double outlet right ventricle, an atrial septal defect and dextrocardia were seen in 5 patients (24 % ). Four patients survived. Seventeen died, 12 from sepsis or septic shock. Autopsies were performed on 10 patients. All of the ectopia cordis patients died. Pentalogy of Cantrell is uncommon, and its association with ectopia cordis indicates poor prognosis.