Malignant nerve sheath tumor involving glossopharyngeal, vagus and spinal nerve with intracranial-extracranial extension and systemic metastases in a patient with type 1 neurofibromatosis: A case report

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• 作者：José ; Raú ; l Guerra-Mora^a ; ^b ; ^{drjrgm@hotmail.com} ; Juan D. Del Castillo-Calcá ; neo^a ; ^b ; Marí ; a Elena Có ; rdoba-Mosqueda^a ; ^b ; Jorge Yá ; ñ ; ez-Castro^a ; ^b ; Ulises Garcí ; a-Gonzá ; lez^a ; ^b ; Eduardo Soriano-Navarro^d ; Leticia Llamas-Ceras^c ; Rosa Marí ; a Vicuñ ; a-Gonzá ; lez^c
• 关键词：Malignant peripheral nerve sheath tumor ; Neurofibromatosis ; Glossopharyngeal ; Vagus ; Spinal ; Villaret&rsquo ; s syndrome
• 刊名：International Journal of Surgery Case Reports
• 出版年：2016
• 出版时间：2016
• 年：2016
• 卷：29
• 期：Complete
• 页码：196-200
• 全文大小：1936 K
• 卷排序：29

文摘

Intracranial malignant peripheral nerve sheath tumors are an extremely rare pathology with a high morbidity and mortality. The most frequently affected cranial nerves in decreasing order of frequency are the trigeminal, vestibulocochlear and facial, being glossopharyngeal, vagus and spinal nerves extremely rare affected. This manuscript is the first in English-written literature to expose the case of an adult female patient with NF1 who presented a MPNST involving the glossopharyngeal, vagus and spinal left nerves with intracranial-extracranial extension and systemic metastases. Treatment strategies for this particular pathology are still unclear due to the low frequency of the disease and a lack of number of cases, making them a challenge for the neurosurgeon.