Laryngite pseudo-membraneuse sévère dans le cadre d’une épidermolyse bulleuse acquise
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- 作者：H. Lecomte ; M. Folia ; G. Muller ; D. Gilbert ; F. Tron ; J.-F. Besancenot ; P. Romanet
- 关键词：Epidermolysis bullosa acquisita ; Laryngitis
- 刊名：La Revue de Medecine Interne
- 出版年：2010
- 出版时间：May 2010
- 年：2010
- 卷：31
- 期：5
- 页码：e7-e10
- 全文大小：441 K
文摘
Epidermolysis bullosa acquisita is a rare entity belonging to the auto-immune cutaneous blistering disorders of the dermo-epidermal junction. Clinical manifestations are generally cutaneous including the development of sub-epidermal blisters. Mucosal manifestations should be systematically looking for, but laryngeal involvement remains uncommon. We report an 81-year-old woman who presented with dysphagia, dyspnea and dysphonia as the presenting features of laryngeal involvement of an epidermolysis bullosa acquisita. This is the tenth reported case in the literature. We describe our diagnostic approach and the therapeutic management, comparing them with the literature.