- 作者：Gianantonio MANZONI ; Philip GODDARD RANSLEY
- 刊名：Journal of Pediatric Urology
- 出版年：2007
- 出版时间：April 2007
- 年：2007
- 卷：3
- 期：Supplement 1
- 页码：S90
- 全文大小：30 K
PURPOSE
Isolated female epispadias, without bladder exstrophy involvement, is an exceedingly rare congenital malformation with a reported incidence varying between 1/160.000 to 1/480.000. The diagnosis is often overlooked due to failure to recognise the cardinal features of a bifid clitoris and patulous urethral opening.MATERIAL AND METHODS
Classically, female epispadias is associated with urinary incontinence with an incompletely formed bladder neck and a short, wide urethra. One strategy for repair is to combine external cosmetic correction with urethral reduction and angulation performed from the perineum. In some cases this may be all that is required for achieving satisfactory voiding continence. In others further surgical intervention is required at the bladder neck, but this initial procedure increases outflow resistance and stimulates the development of bladder capacity which in turn facilitates any continence surgery at the bladder neck which may be required.
RESULTS
In this video we demonstrate the primary surgical repair of an isolated epispadias in a 9 month old female, including:
1. Urethral reduction.
2. Repair of the “urogenital diaphragm”.
3. Urethral angulation.
4. Clitoroplasty and labioplasty.