Further evidence of the etiology of prune belly syndrome provided by a transient massive intraabdominal cyst in a female

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• 作者：Uddaka S. Wijesinghe^a ; ^{uddakas@gmail.com" class="auth_mail" title="E-mail the corresponding author} ; Mathievathaniy Muthucumaru^b ; Spencer W. Beasley^b
• 关键词：Prune belly syndrome (PBS) ; Etiology ; Pathogenesis ; Fetal cyst
• 刊名：Journal of Pediatric Surgery
• 出版年：2016
• 出版时间：August 2016
• 年：2016
• 卷：51
• 期：8
• 页码：1390-1393
• 全文大小：1080 K

文摘

We present a female neonate born with prune belly syndrome (PBS) in whom a large intraabdominal cyst was diagnosed at 12 weeks of gestation. Rapid and exponential growth of the cyst caused pressure effects on the intraabdominal organs and stretching of the anterior abdominal wall by 19 weeks of gestation. This led to drainage of the massive cyst at 20 weeks of gestation to prevent fetal demise. This case provides further clues to the likely etiology of PBS: transient stretching and attenuation of the fetal abdominal wall secondary to gross fetal abdominal distension – from any cause.