Idiopathic interstitial pneumonia-associated pulmonary hypertension: A target for therapy?

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• 作者：Steven D. Nathan^a ; ^{Steven.Nathan@inova.org} ; Jü ; rgen Behr^b ; Vincent Cottin^c ; Harold R. Collard^d ; Marius M. Hoeper^e ; Fernando J. Martinez^f ; Athol U. Wells^g
• 关键词：Idiopathic interstitial pneumonia ; Interstitial lung disease ; Pulmonary hypertension ; Idiopathic pulmonary fibrosis
• 刊名：Respiratory Medicine
• 出版年：2017
• 出版时间：January 2017
• 年：2017
• 卷：122
• 期：supp_S1
• 页码：S10-S13
• 全文大小：211 K
• 卷排序：122

文摘

IIPs involve varying combinations of fibrosis and inflammation of unknown cause. IIPs appear to follow a similar course once PH supervenes. Exploring PH drugs in broadly defined IIP, rather than exploring only specific subtypes, such as IPF, may be of benefit. RISE-IIP looked to validate riociguat in patient with IIP-PH in a randomized trial.