Interstitial lung disease and myositis-specific and associated autoantibodies: Clinical manifestations, survival and the performance of the new ATS/ERS criteria for interstitial pneumonia with autoimmune features (IPAF)
文摘
Patients differ in clinical manifestations according to the autoantibody profile. Only 50% of the patients fulfilled BPC. However, those patients that did not fulfill BPC, were classified as IPAF. There was no difference in survival among BPC and IPAF patients. Jo-1 patients had a better survival and mortality was associated to the extent of lung inflammation.