Anesthetic implications of Parry Romberg Syndrome: A case report

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• 作者：Guiomar Ferná ; ndez-Castellano^a ; ^{guio012@hotmail.com} ; Rosana Guerrero-Domí ; nguez^b ; Daniel Ló ; pez-Herrera-Rodrí ; guez^b ; Ignacio Jim&eacute ; nez^c
• 关键词：Laryngoscopy ; Anesthesia ; Airway management ; Facial hemiatrophy ; Craniofacial dysostosis
• 刊名：Colombian Journal of Anesthesiology
• 出版年：2017
• 出版时间：January 2017
• 年：2017
• 卷：45
• 期：supp_S1
• 页码：26-30
• 全文大小：694 K
• 卷排序：45

文摘

Parry–Romberg Syndrome is a rare degenerative disease characterized by unilateral atrophy affecting the skin, connective tissue, muscle and bone. The end result is facial asymmetry associated with other skin, dental, visual, cardiovascular, and neurological disorders.Clinical findings, diagnostic evaluation and interventionsThe case of a patient with Parry–Romberg Syndrome programmed for frontonasal flap remodeling is discussed. The patient's history includes trigeminal neuralgia, epilepsy, and two previous surgical interventions. Uneventful endotracheal intubation with the Glideoscope® video laryngoscope was performed, upon adequate pre-oxygenation followed by anesthetic induction.ConclusionThe phenotypical characteristics of Parry Romberg Syndrome are severe facial hemiatrophy and craniofacial anomalies that require careful preoperative evaluation and management of a potentially difficult airway. Consequently, the use of video laryngoscopes is a first-line approach. Due to the syndrome's associated disorders, it is essential to maintain hemodynamic stability and prevent any potential seizures.