The role of operative intervention in management of congenital extrahepatic portosystemic shunt

详细信息    查看全文

• 作者：Yukihiro Sanada ; MD^a ; ^{yuki371@jichi.ac.jp} ; Taizen Urahashi ; MD ; PhD^a ; Yoshiyuki Ihara ; MD ; PhD^a ; Taiichi Wakiya ; MD^a ; Noriki Okada ; MD^a ; Naoya Yamada ; MD^a ; Satoshi Egami ; MD^a ; Shuji Hishikawa ; MD ; PhD^a ; Youichi Kawano ; MD ; PhD^a ; Kentaro Ushijima ; PhD^b ; Shinya Otomo^c ; Koichi Sakamoto ; PhD^c ; Manabu Nakata ; MD ; PhD^d ; Yoshikazu Yasuda ; MD ; PhD^e ; Koichi Mizuta ; MD ; PhD^a
• 刊名：Surgery
• 出版年：2012
• 出版时间：March 2012
• 年：2012
• 卷：151
• 期：3
• 页码：404-411
• 全文大小：453 K

文摘

| Figures/TablesFigures/Tables | ReferencesReferences

Background and Aims

Congenital extrahepatic portosystemic shunt (CEPS) is a rare venous malformation in which mesenteric venous blood drains directly into the systemic circulation. It is still a matter of debate whether conservative or operative strategies should be used to treat symptomatic CEPS. The aim of this study was to evaluate the role of operative intervention in the management of CEPS.

Methods

Between June 2004 and August 2010, 6 consecutive patients with symptomatic CEPS were treated in our department. There were 3 male and 3 female patients, with a median age of 3.5 years (range, 1-8). Their demographic, clinical, and laboratory data were analyzed. All patients were scheduled to undergo shunt ligation or liver transplantation (LT).

Results

Living donor LT was carried out in 4 patients, and shunt ligation in 2. After a median follow-up of 25 months, all the patients are alive currently with marked relief of symptoms.

Conclusion

Shunt ligation or LT for symptomatic CEPS is potentially curative.