Surgical management of Gorham disease involving the upper cervical spine with occipito-cervical-thoracic fusion: a case report

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• 作者：Adam Schell ; MD^a ; John M. Rhee ; MD^b ; ^{john.rhee@emory.org" class="auth_mail" title="E-mail the corresponding author} ; Abigail Allen ; MD^c ; Lindsay Andras ; MD^d ; Feifei Zhou ; MD^b ; ^e
• 刊名：The Spine Journal
• 出版年：2016
• 出版时间：July 2016
• 年：2016
• 卷：16
• 期：7
• 页码：e467-e472
• 全文大小：1006 K

文摘

Gorham disease is a rare osteolytic condition, with only 17 reported cases primarily affecting the cervical spine.

Purpose

We report the case of a 31-year-old woman with severe kyphotic instability and myelopathy of the upper cervical spine secondary to massive osteolysis of the posterior elements. The surgical management, clinical outcome, and review of the relevant literature are discussed.

Study Design

This is a case report and a literature review.

Patient Sample

This is a report of one patient with Gorham disease of the cervical spine.

Methods

We report the case of a 31-year-old woman with Gorham disease affecting the upper cervical spine. Combined posterior and anterior stabilization and fusion was performed from the occiput to the thoracic spine.

Results

Six-year follow-up with annual computed tomography imaging showed solid fusion from the occiput to T2. No spread or local recurrence has developed to date.

Conclusions

Correction of severe instability with myelopathy due to Gorham disease of the upper cervical spine was achieved through posterior and anterior occipito-cervical-thoracic fusion.