Cardiomyopathy Phenotypes and Outcomes for Children With Left Ventricular Myocardial Noncompaction: Results From the Pediatric Cardiomyopathy Registry

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• 作者：John L. Jefferies ; MD ; MPH¹ ; ^{john.jefferies@cchmc.org" class="auth_mail" title="E-mail the corresponding author} ; James D. Wilkinson ; MD ; MPH² ; ³ ; Lynn A. Sleeper ; ScD⁴ ; Steven D. Colan ; MD⁵ ; Minmin Lu ; MS⁴ ; Elfriede Pahl ; MD⁶ ; Paul F. Kantor ; MBBCh⁷ ; Melanie D. Everitt ; MD⁸ ; Steven A. Webber ; MBChB⁹ ; Beth D. Kaufman ; MD¹⁰ ; Jacqueline M. Lamour ; MD¹¹ ; Charles E. Canter ; MD¹² ; Daphne T. Hsu ; MD¹¹ ; Linda J. Addonizio ; MD¹³ ; Steven E. Lipshultz ; MD³ ; ¹⁴ ; Jeffrey A. Towbin ; MD¹ ; ¹⁵ ; on behalf of the Pediatric Cardiomyopathy Registry Investigators
• 关键词：Cardiomyopathy ; pediatrics ; heart failure
• 刊名：Journal of Cardiac Failure
• 出版年：2015
• 出版时间：November 2015
• 年：2015
• 卷：21
• 期：11
• 页码：877-884
• 全文大小：685 K

文摘

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d="p0010">LVNC is present in at least 5% of children with cardiomyopathy.

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d="p0015">The concurrent phenotype seen in association with LVNC predicts outcome.

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d="p0020">The survival rate of children with LVNC and the HCM phenotype was lower than that of published reports of children with pure HCM.

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d="p0025">In children with the isolated form of LVNC, 6% die or undergo cardiac transplantation in the first 5 years after diagnosis.

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