- 作者：Debora Luciano ; Daniela Laux ; Younes Boudjemline ; S茅bastien Hasco毛t ; Jean-Ren茅 Lusson ; Clio Sorensen ; Caroline Ovaert ; Bernard Kreitmann ; Richard Van Praagh ; Alain Fraisse
- 关键词：Congenital heart disease ; Intervention ; Pulmonary vein
- 刊名：International Journal of Cardiology
- 出版年：10 December, 2013
- 年：2013
- 卷：170
- 期：2
- 页码：221-226
- 全文大小：614 K
Background
A persistent anastomosis between the pulmonary veins that connect with the left atrium and the systemic vein that drains into the right atrium has occasionally been reported. We report characteristics and transcatheter therapy in partially abnormal pulmonary venous return with additional drainage to the left atrium.Methods
We retrospectively studied such patients in 5 institutions.
Results
Ten patients (6 girls) presented at a median age of 8 (0.1 to 54) years with 2 anatomic types: 8 vertical vein types with drainage of the left upper lobe to the innominate vein via a large vertical vein (left superior cardinal vein) and to the left atrium via the left upper pulmonary vein; and 2 scimitar vein (SV) types with drainage of the right middle and lower pulmonary veins into the inferior vena cava and to the left atrium via an anomalous connecting vein. Associated malformations were aortic coarctation (n = 2) and secundum atrial septal defects (n = 3). Two patients of the vertical vein type were operated. Transcatheter occlusion of the abnormal pulmonary venous return was performed in 7 cases, associated with occlusion of systemic arterial supply (n = 2), secundum atrial septal closure (n = 2), left upper pulmonary vein stenosis stenting (n = 1), and coarctation stenting (n = 1). Including previously published cases, 18 patients (13 vertical veins and 5 scimitar veins) underwent transcatheter repair. Patients over 40 years of age tend to be symptomatic at presentation (p = 0.056).
Conclusion
In partially abnormal pulmonary venous return with dual drainage, transcatheter therapy can be offered in the majority of patients.