Successful pregnancy and delivery in a woman with a single ventricle and eisenmenger syndrome

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• 作者：Marouane Boukhris ; Kaouathar Hakim ; Fatma Ouarda ; Hela M&rsquo ; saad ; Rafik Boussaada
• 刊名：Journal of the Saudi Heart Association
• 出版年：2013
• 出版时间：April, 2013
• 年：2013
• 卷：25
• 期：2
• 页码：110
• 全文大小：42 K

文摘

The single ventricle is a rare abnormality found in 1 % of patients with congenital heart disease, often discovered during the childhood. Without pulmonary stenosis, the disease can progress to a fixed pulmonary hypertension. Both pregnancy and delivery are risky events apt to increase the right to left shunt.

The presence of pulmonary hypertension is considered to be the major maternal risk factor. Therefore, pregnancy is contraindicated.

We reported the case of a 27-year-old woman with a single ventricle without pulmonary protection and fixed pulmonary hypertension at 60 mm Hg, discovered during a pregnancy. The management of the caesarean delivery was successfully done by a regional anesthesia and nitric oxide. The outcome was good under anticoagulation therapy and then under inhibitors of endothelin receptors.

Even if they were contraindicated, pregnancy and delivery were successfully achieved in this patient. The revaluation of ventricular function and pulmonary blood pressure would provide information about the long-term prognosis