Weber–Christian disease presenting with retroperitoneal panniculitis

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• 作者：Motoki Nakai ; Morio Sato ; Shinya Sahara ; Yumiko Ibata ; Katsuhiko Higashi ; Masako Maeda ; Masashi Kimura ; Masaki Terada
• 关键词：Weber– ; Christian disease ; Retroperitoneal panniculitis ; ⁶⁷Ga scintigraphy ; Nodular erythema
• 刊名：European Journal of Radiology Extra
• 出版年：2006
• 出版时间：December 2006
• 年：2006
• 卷：60
• 期：3
• 页码：89-92
• 全文大小：1010 K

文摘

A 30-year-old female was admitted to our hospital for fever and epigastric pain. Hematology showed increases in the leukocyte count, CRP level, and erythrocyte sedimentation rate. Multiple nodular erythemas with tenderness in the limbs, arthralgia, and hepatosplenomegaly were noted. Abdominal CT and MRI revealed retroperitoneal panniculitis. ⁶⁷Ga scintigraphy showed abnormal accumulations in the nodular erythema regions and in the retroperitoneal region. A biopsy of a subcutaneous nodule led to the diagnosis of Weber–Christian disease (WCD). Steroid therapy resulted in the disappearance of these symptoms. In addition, the abnormal accumulations on ⁶⁷Ga scintigraphy and the abnormal CT findings also disappeared. ⁶⁷Ga scintigraphy was useful for evaluating the treatment response. There has been no case report of Weber–Christian disease with retroperitoneal panniculitis visualized on CT, MRI, and ⁶⁷Ga scintigraphy.