Composite pheochromocytoma with a malignant peripheral nerve sheath tumor: Case report and review of the literature

详细信息    查看全文

• 作者：Takeshi Namekawa^a ; Takanobu Utsumi^a ; ^{p-cats@pd6.so-net.ne.jp" class="auth_mail" title="E-mail the corresponding author} ; Takashi Imamoto^a ; Koji Kawamura^a ; Takashi Oide^b ; Tomoaki Tanaka^c ; Naoki Nihei^a ; Hiroyoshi Suzuki^d ; Yukio Nakatani^b ; Tomohiko Ichikawa^a
• 关键词：adrenalectomy ; adrenal tumor ; malignant peripheral nerve sheath tumor ; pheochromocytoma ; spontaneous rupture
• 刊名：Asian Journal of Surgery
• 出版年：2016
• 出版时间：July 2016
• 年：2016
• 卷：39
• 期：3
• 页码：187-190
• 全文大小：836 K

文摘

Adrenal tumors with more than one cellular component are uncommon. Furthermore, an adrenal tumor composed of a pheochromocytoma and a malignant peripheral nerve sheath tumor is extremely rare. A composite pheochromocytoma with malignant peripheral nerve sheath tumor in a 42-year-old man is reported here. After adequate preoperative control, left adrenalectomy was performed simultaneously with resection of the ipsilateral kidney for spontaneous rupture of the left adrenal tumor. Pathological findings demonstrated pheochromocytoma and malignant peripheral nerve sheath tumor in a ruptured adrenal tumor. To date, there have been only four reported cases of composite pheochromocytoma with malignant peripheral nerve sheath tumor, so the present case is only the fifth case in the world. Despite the very poor prognosis of patients with pheochromocytoma and malignant peripheral nerve sheath tumors reported in the literature, the patient remains well without evidence of recurrence or new metastatic lesions at 36 months postoperatively.