Type 1 Neurofibromatosis is an autosomal disorder associated with gastrointestinal tumors in almost one quarter of the cases.
The presence of synchronous malignant gastrintestinal tumor in patients with type 1 Neurofibromatosis is rarely reported in the literature.
Patients with type 1 Neurofibromatosis with gastrointestinal complaints should be thoroughly evaluated to rule out malignancy.
Optimal management of patients with synchronous neoplasms is single-stage surgical resection.