We present a case of a 12 year-old girl, who had a painful head tilt. She had no history of trauma or pre-existing bone disease; contrast computed tomography of the neck revealed a significant C1-C2 rotary subluxation. Our patient needed to be treated with an arthrodesis C1-C2.
Grisel's syndrome is a rare but well-documented clinical entity. It is a nontraumatic, fixed rotary subluxation of C1 on C2 (atlantoaxial). Although first described in 1830, the exact mechanism of Grisel's syndrome remains unclear.
Patients typically present with a painful torticollis, possible history of fever, and other non-specific signs of infection.
Children who have a hypermobility of C1 on C2 are at risk for Grisel's syndrome following any kind of inflammatory, infectious, or postoperative process in the head and neck.
Patients with Grisel's syndrome can have catastrophic outcomes, but prompt diagnosis and proper treatment significantly improve the chances for full functional recovery.