Rosai-Dorfman disease with exclusive intra-abdominal lymphadenopathy masquerading as Wilkie鈥檚 syndrome

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• 作者：Tarique Hussain Ashraf^a ; Abhijit Chandra^a ; ^{tarique536@yahoo.co.in" class="auth_mail} ; Ramendra K. Jauhari^b ; Sunil Kumar Singh^a ; M. Noushif^a
• 关键词：Rosai&ndash ; Dorfman disease ; Wilkie&rsquo ; s syndrome ; Lymphadenopathy ; Histiocytosis
• 刊名：Arab Journal of Gastroenterology
• 出版年：March, 2014
• 年：2014
• 卷：15
• 期：1
• 页码：40-41
• 全文大小：588 K

文摘

Rosai-Dorfman disease is a rare histiocytic proliferative disorder with a distinctive microscopic appearance. Patients usually present with nonspecific symptoms and massive cervical lymphadenopathy. Exclusive involvement of intra-abdominal lymph nodes is unusual and presentation mimicking Wilkie鈥檚 syndrome due to compression of the third part of the duodenum by enlarged retroduodenal lymph nodes is rare. This entity should be included in the differential diagnosis with infectious, granulomatous and malignant causes of intra-abdominal lymphadenopathy. We highlight an uncommon presentation and discuss the challenges in the diagnosis and management of Rosai-Dorfman disease.