Staged Fontan's operation for unguarded tricuspid orifice with pulmonary atresia

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• 作者：Masanori Hirota ; Masaaki Kawada ; Kozo Ishino ; Shunji Sano
• 关键词：CHD ; Cyanotic ; Fontan ; Tricuspid valve
• 刊名：European Journal of Cardio-Thoracic Surgery
• 出版年：2008
• 出版时间：November 2008
• 年：2008
• 卷：34
• 期：5
• 页码：1111-1112
• 全文大小：264 K

文摘

We report a rare case of unguarded tricuspid orifice with pulmonary atresia, which is devoid of any guarding valvular tissue at tricuspid annulus. A left Blalock–Taussig shunt was constructed on the 17th day of life. At 4 years of age, a bidirectional Glenn's operation was performed for the further growth of the pulmonary bed and the volume reduction of the left ventricle. Finally, an extracardiac cavo-pulmonary connection was created using a ringed Gore-Tex graft at 6 years of age. Staged Fontan's strategy may contribute to a good surgical outcome for this highly lethal anomaly.