Herlyn-Werner-Wunderlich Syndrome Consisting of Uterine Didelphys, Obstructed Hemivagina and Ipsilateral Renal Agenesis in a Newborn

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• 作者：Tsung-Hsin Wu^a ; Trang-Tiau Wu^b ; ^c ; Yan-Yan Ng^a ; Soo-Cheen Ng^c ; ^d ; Pen-Hua Su^a ; ^c ; ^{jen@csh.org.tw} ; Jia-Yuh Chen^a ; ^c ; Suh-Jen Chen^a
• 关键词：hemivagina ; Herlyn-Werner-Wunderlich (HWW) syndrome ; ipsilateral renal agenesis ; uterine didelphys
• 刊名：Pediatrics Neonatology
• 出版年：2012
• 出版时间：February 2012
• 年：2012
• 卷：53
• 期：1
• 页码：68-71
• 全文大小：677 K

文摘

Herlyn-Werner-Wunderlich (HWW) syndrome is a rare variant of M¨¹llerian duct anomalies consisting of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. Patients with HWW syndrome are usually asymptomatic until menarche, when they present with acute lower abdominal pain. Here we report a case of a female newborn with right renal agenesis diagnosed during the pregnancy. The patient presented with a protruding mass over the vaginal introitus that was associated with an obstructed hemivagina and uterine didelphys.