Spontaneous biloma in the presence of an intrahepatic cholangiocarcinoma is an extremely rare situation. Spontaneous rupture of bile vessels due an intrahepatic cholangiocarcinoma is an urgent and life-threatening complication. This is the first case treated with a left hepatectomy and also the first one to report such a long disease-free survival. Spontaneous bilomas should be considered in patients presented with epigastric pain, hepatic tumor and fluid collection.