Melorheostosis with recurrent soft-tissue components: a histologically confirmed case

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• 作者：Shoichi Hasegawa ; Shotaro Kanda ; Hiroki Imada ; Takehiko Yamaguchi…
• 关键词：Melorheostosis ; Soft ; tissue component ; Pathological confirmation ; Surgical treatment
• 刊名：Skeletal Radiology
• 出版年：2017
• 出版时间：March 2017
• 年：2017
• 卷：46
• 期：3
• 页码：399-404
• 全文大小：
• 刊物类别：Medicine
• 刊物主题：Imaging / Radiology; Orthopedics; Pathology; Nuclear Medicine;
• 出版者：Springer Berlin Heidelberg
• ISSN：1432-2161
• 卷排序：46

文摘

Melorheostosis is a very rare disorder characterized by irregular cortical thickening seen on radiographs. In this paper, we present a case of melorheostosis with microscopically confirmed soft-tissue components. The patient was a 51-year-old man who complained of severe pain in the lateral aspect of his right knee. The excision of an ossified soft-tissue lesion relieved intractable pain that had lasted 20 years. Microscopically, the cortex of the affected fibula was composed of thick compact bone and the soft-tissue component consisted of dense compact bone without endochondral ossification. The presence of soft-tissue osseous nodules around the joints is one of the specific conditions for melorheostosis and should be differentiated from synovial chondromatosis. The ossified soft-tissue lesion in our patient is to our knowledge the first reported case of the histologically confirmed soft-tissue component of melorheostosis, which differs from that of synovial chondromatosis.