Radiological imaging of congenital hand anomalies—a 6-year single-centre experience and what the hand surgeons want to know

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• 作者：E.-L. Gerety ; I. Grant ; M. A. Hopper
• 关键词：Hand anomalies ; Paediatrics ; Polydactyly ; Syndactyly ; Thumb hypoplasia
• 刊名：Skeletal Radiology
• 出版年：2015
• 出版时间：April 2015
• 年：2015
• 卷：44
• 期：4
• 页码：549-556
• 全文大小：1,118 KB
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• 刊物类别：Medicine
• 刊物主题：Medicine & Public Health
  Imaging and Radiology
  Orthopedics
  Pathology
  Nuclear Medicine
  
• 出版者：Springer Berlin / Heidelberg
• ISSN：1432-2161

文摘

Objective Congenital hand anomalies present a rare but important physical and emotional challenge for children and parents. Radiological imaging is important for accurate diagnosis, to aid decision making and to monitor changes in the growing hand. The goal of any treatment is to help the child achieve his/her maximum potential, to provide a useful hand with attention to cosmesis. We investigated the range of congenital hand anomalies imaged in a tertiary referral centre. We examined the timing of imaging and the key clinical questions. Methods The radiology imaging system was searched retrospectively for radiographs of congenital hand anomalies over a 6-year period. The images were reviewed and patient demographics, diagnosis and other imaging recorded. Results Over 6?years, 85 patients had imaging. Twenty-three patients had bilateral problems and 11 had recognised syndromes. The most common abnormalities imaged were duplicated thumbs (28?%), followed by syndactyly (18?%). Children were first imaged as early as 1?day old, with the median age of initial imaging 12?months. Conclusions Thumb duplication and syndactyly are the most common conditions for which radiographs are requested at our hospital, although overall syndactyly is considered the most common congenital hand anomaly. For a variety of reasons, children are often imaged very early, before review by the Specialist in Children’s Hand Surgery (despite surgery being unlikely before 1?year of age.) We discuss the classification systems and specific issues that hand surgeons want to know from the radiologists.