Konnatale Fehlbildungen des weiblichen Genitaltrakts

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• 作者：K. Heusinger ; PD Dr. P. G. Oppelt
• 关键词：Störungen der Geschlechtsentwicklung ; Embryonale Entwicklung ; Pubertät ; Hämatokolpos ; Sexuelle Differenzierung ; Disorders of sex development ; Embryonic development ; Puberty ; Hematocolpos ; Sex differentiation
• 刊名：Der Gyn?kologe
• 出版年：2016
• 出版时间：February 2016
• 年：2016
• 卷：49
• 期：2
• 页码：79-86
• 全文大小：596 KB
• 参考文献：1.Adachi M, Takayanagi R, Tomura A, Imasaki K, Kato S, Goto K, Yanase T, Ikuyama S, Nawata H (2000) Androgen-insensitivity syndrome as a possible coactivator disease. N Engl J Med 343:856–862. doi:10.1056/NEJM200009213431205CrossRef PubMed
  2.Brucker SY, Oppelt P, Ludwig KS (2005) Vaginale und uterine Fehlbildungen Teil 2. Geburtshilfe Frauenheilkd 65:R221–R244CrossRef
  3.Oppelt PG (2008) Feminine Entwicklung (Ovarien, Uterus, Mamma). In: Ranke R, Dörr HG (Hrsg) Hypogonadismus in der Adoleszenz. Verlag wissentschaftliche Skripten, Zwickau, S 13–16
  4.Reddy J, Laufer MR (2010) Hypertrophic labia minora. J Pediatr Adolesc Gynecol 23:3–6. doi:10.1016/j.jpag.2009.01.071CrossRef PubMed
  5.Rock JA, Zacur HA, Dlugi AM, Jones HW Jr, TeLinde RW (1982) Pregnancy success following surgical correction of imperforate hymen and complete transverse vaginal septum. Obstet Gynecol 59:448–451PubMed
  6.Oppelt PG, Dörr H-G (2015) Kinder- und Jugendgynäkologie, 1. Aufl. Thieme, Stuttgart
  
• 作者单位：K. Heusinger (1) (2)
  PD Dr. P. G. Oppelt (1) (2)
  
  1. Frauenklinik des Universitätsklinikums Erlangen, Friedrich-Alexander-Universität Erlangen-Nürnberg, Universitätsstraße 21–23, 91054, Erlangen, Deutschland
  2. Universitäts-Fortpflanzungszentrum Franken, Erlangen, Deutschland
  
• 刊物主题：Gynecology; Obstetrics/Perinatology; Endocrinology;
• 出版者：Springer Berlin Heidelberg
• ISSN：1433-0393

文摘

Congenital anomalies of the female genital tract include anomalies of the outer genital organs (mons pubis, clitoris including praeputium clitorides, labia majora et minora, ostium urethrae externum, hymen and vestibulum vaginae) as well as inner genital organs (cervix, corpus uteri and the adnex). Pathologies and norm variants are sometimes not easy to distinguish from each other. Knowledge about physical developmental stages and their timing (especially pubarche, telarche and menarche) is necessary as well as knowledge about the embryonal development of the genital organs to correctly diagnose congenital anomalies of the female genital tract. Most diagnoses can be made after a comprehensive assessment of the medical history, examination of the outer and inner genital organs and an abdominal ultrasound. Congenital anomalies of the female genital tract can have an influence on quality of life, sexuality and fertility. Early diagnosis can prevent a relevant number of complications like hematocolpos and hematometra. In this article standard methods for the diagnosis of congenital anomalies of the female genital tract are described. Keywords Disorders of sex development Embryonic development Puberty Hematocolpos Sex differentiation