Primary Hepatic Ewing’s Sarcoma with Cytogenetic Confirmation

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• 作者：P. F. McGrann (1)
  I. J. Pooleman (1)
  C. H. Wilson (1)
  B. Haugk (2)
  J. Scott (3)
  R. M. Charnley (1)
  
• 关键词：Ewing’s sarcoma ; Hepatic mass ; Cytogenetic diagnosis
• 刊名：Journal of Gastrointestinal Surgery
• 出版年：2014
• 出版时间：March 2014
• 年：2014
• 卷：18
• 期：3
• 页码：635-637
• 全文大小：258 KB
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• 作者单位：P. F. McGrann (1)
  I. J. Pooleman (1)
  C. H. Wilson (1)
  B. Haugk (2)
  J. Scott (3)
  R. M. Charnley (1)
  
  1. Department of Hepatopancreaticobiliary Surgery, The Freeman Hospital, Freeman Road, High Heaton, Newcastle upon Tyne, UK, NE7 7DN
  2. Department of Cellular Pathology, The Royal Victoria Infirmary, Newcastle upon Tyne, UK
  3. Department of Radiology, The Freeman Hospital, Newcastle upon Tyne, UK
  
• ISSN：1873-4626

文摘

Introduction Extraskeletal Ewing’s sarcoma is reported in the medical literature, but none has been described as presenting with a resectable liver mass. Methods A case of a 29-year-old male patient who presented with a large symptomatic mass in the right lobe of the liver which, following resection, demonstrated the characteristic histopathology and fusion protein (EWSR1-Fli1) found in Ewing’s sarcoma was reported. Discussion Complete surgical resection offers the best long-term outlook. Cure rates with appropriate surgical and chemotherapeutic management range between 30 and 60 %.