Male cloaca malformation: rare variant of anorectal malformation

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• 作者：Shilpa Sharma ; Devendra K. Gupta
• 关键词：Male Cloaca ; Posterior sagittal anorectourethroplasty ; Urethrostomy ; Anorectal malformation
• 刊名：Pediatric Surgery International
• 出版年：2015
• 出版时间：August 2015
• 年：2015
• 卷：31
• 期：8
• 页码：747-752
• 全文大小：938 KB
• 参考文献：1.Livingston JC, Elicevik M, Breech L, Crombleholme TM, Pe?a A, Levitt MA (2012) Persistent cloaca: a 10-year review of prenatal diagnosis. J Ultrasound Med 31:403-07PubMed
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• 作者单位：Shilpa Sharma (1)
  Devendra K. Gupta (1)
  
  1. Department of Pediatric Surgery, All India Institute of Medical Sciences, New Delhi, India
  
• 刊物类别：Medicine
• 刊物主题：Medicine & Public Health
  Pediatrics
  Surgery
  Pediatric Surgery
  
• 出版者：Springer Berlin / Heidelberg
• ISSN：1437-9813

文摘

Purpose Experience with male cloaca (MC), a single opening in perineum for passage of urine and meconeum is described. Methods Cases of MC were ambispectively studied, prospectively from July 2007 to April 2015 and retrospectively for last three decades. Results Seven cases of MC were identified, between the ages of newborn-?years (median 10?days). Two missed cases underwent a colostomy, posterior sagittal anorectoplasty, and urethroplasty. Two cases underwent perineal urethrostomy and anoplasty followed by urethroplasty. In one case, part of the rectal wall was used to form urethral tube and urethrostomy. For three recent cases, posterior sagittal anorectourethroplasty was done with mobilization of rectal pouch and common channel, separation of common wall between the urethra and rectum, urethroplasty varying from 1.5 to 3?cm, perineal body reconstruction, perineal urethrostomy and anoplasty. Follow-up of 6 patients varied from 3?months to 23?years. One case is lost to follow-up. Three patients have completed repair. Complications included a discharging sinus and a urethral fistula in one case each. One patient died while awaiting urethroplasty. Two patients are awaiting formal urethroplasty. Conclusion With familiarity of varying anatomy of MC, early recognition can avoid a neonatal colostomy in selected patients.