PEComa of the uterus with coexistence of situs inversus totalis, a case report and literature review

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• 作者：Yang Han ; Ting-ting Liu ; Xue-shan Qiu ; Qing-chang Li ; Yi Zhao…
• 关键词：PEComa ; Uterus ; Situs inversus totalis
• 刊名：Diagnostic Pathology
• 出版年：2015
• 出版时间：December 2015
• 年：2015
• 卷：10
• 期：1
• 全文大小：1,981 KB
• 刊物主题：Pathology;
• 出版者：BioMed Central
• ISSN：1746-1596

文摘

PEComas are a group of very rare mesenchymal neoplasms, which express myogenic and melanocytic markers, such as HMB-45 and actin. Situs inversus totalis represents a complete left to right side transposition of the asymmetrical thoracic and abdominal organs and incorporates dextrocardia. The presence of uterus PEComa in the setting of situs inversus totalis is extremely rare. Here, we report a case of PEComa of uterus with coexistence of situs inversus totalis and review the literatures. To the best of our knowledge this is the fist report of a uterus PEComa patient with situs inversus totalis.