文摘
Objective This study reviewed surgical outcomes of staged repair for complete atrioventricular septal defect with tetralogy of Fallot, especially with focusing on the post-operative left-sided atrioventricular valve function. Methods Between 1992 and 2013, 10 patients with complete atrioventricular septal defect with tetralogy of Fallot underwent total correction by the following surgical strategy. Systemic-to-pulmonary shunt was placed at first at the mean age of 1.5?±?1.3?months. Then confirming sufficient development of the left heart structures, the total correction was performed at the mean age of 1.4?±?0.6?years. Second shunt was required in 4 (40?%) patients to develop the left heart structures. Results The left ventricular end-diastolic volume before total correction was 127?±?30?% of normal size. The two-patch repair was applied in 8 (80?%) patients. There was no mortality, and 1 reoperation case for left-sided atrioventricular valve regurgitation. The follow-up was completed on all patients and the mean follow-up period was 7.4?±?7.0?years. The post-operative left-sided atrioventricular valve regurgitation kept less than moderate for 10-year follow-up in all patients except one patient who required the repair of left-sided atrioventricular valve 1?year after the total correction. Conclusions The post-operative left-sided atrioventricular valve function after the repair of complete atrioventricular septal defect with tetralogy of Fallot maintained with the application of the two-patch repair, early and repeated palliative systemic-to-pulmonary shunt, and the early definitive surgery.