Aortic events in a nationwide Marfan syndrome cohort

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• 作者：Kristian A. Groth ; Kirstine Stochholm ; Hanne Hove…
• 关键词：Epidemiology ; Rare diseases ; Aortic aneurism ; Aortic dissection ; Genetic disease
• 刊名：Clinical Research in Cardiology
• 出版年：2017
• 出版时间：February 2017
• 年：2017
• 卷：106
• 期：2
• 页码：105-112
• 全文大小：
• 刊物主题：Cardiology;
• 出版者：Springer Berlin Heidelberg
• ISSN：1861-0692
• 卷排序：106

文摘

BackgroundMarfan syndrome is associated with morbidity and mortality due to aortic dilatation and dissection. Preventive aortic root replacement has been the standard treatment in Marfan syndrome patients with aortic dilatation. In this study, we present aortic event data from a nationwide Marfan syndrome cohort.