Arnold-Chiari malformation is characterised by prolapse of the cerebellum below the foramen magnum. Type I is frequently diagnosed in adults. Labor poses particular problems in women with this malformation. We present the case of a patient diagnosed during pregnancy, who underwent caesarean delivery under general anesthaesia. A multidisciplinary approach is strongly recommended, decisions must be individualised and firm recommendations cannot be established due to the lack of literature on the topic.