• 作者：Irene Amat Villegas^a ; ^{iamatvil@cfnavarra.es} ; Carmen Lobo Morá ; n^b ; Enrique Zozaya Á ; lvarez^a ; Irene Rodrí ; guez Pé ; rez^a ; Marí ; a del Rosario Mercado Gutié ; rrez^a
• 关键词：Condrosarcoma ; Mesenquimal ; Extraesquelé ; tico ; Carcinoma de cé ; lulas acinares
• 刊名：Revista Espa帽ola de Patolog铆a
• 出版年：2010
• 期刊代码：pca318_16998855
• 类别：med
• 出版时间：October-December 2010
• 卷：43
• 期：4
• 页码：226-228
• 文件大小：1012 K

We present a case of synchronous mesenchymal chondrosarcoma (MC) of the nasopharyx and acinic cell carcinoma (AAC) of the parotid gland in an 11 year old girl. To our knowledge, this is the first time this has been reported.

MC is a high grade sarcoma which is highly aggressive clinically and has a strong tendency towards late recurrences and distant metastases. Morphologically, it is a biphasic tumour made up of areas of small, round, undifferentiated cells intermixed with islands of hyaline cartilage. Typically, it occurs in young adults and requires surgical excision with wide margins.

AAC is an unusual malignant salivary gland neoplasm which can affect a wide age range of patients, from young children to adults. PAS positive cytoplasmic zymogen granules are highly specific for AAC. According to recent studies, malignant salivary gland neoplasms in paediatric patients have a good prognosis.