Quantification of mobility impairment and self-assessment of stiffness in patients with myotonia congenita by the physiotherapist
- 作者：Elisabet Hammaré ; n ; Gunilla Kjellby-Wendt and Christopher Lindberg
- 关键词：Functional measuring instruments ; Self-assessment ; Reliability ; Sensibility to change ; Timed Up& ; Go ; Timed-stands test ; VAS ; BorgCR10 ; Myotonia behaviour scale
- 刊名：Neuromuscular Disorders
- 出版年：2005
- 期刊代码：203_09608966
- 类别：med
- 出版时间：2005
- 卷：15
- 期：9-10
- 页码：610-617
- 文件大小：111 K
摘要
We investigated test–retest reliability and responsiveness in two functional measuring instruments, Timed Up&Go (TUG) and Timed-Stands Test (TST), and in three self-assessment scales, Visual Analogue Scale (VAS), Borg's Category-Ratio Scale (BorgCR10) and Myotonia Behaviour Scale (MBS) when quantifying myotonic stiffness and mobility impairment. These methods were used in the assessment of treatment efficacy of mexiletine. Six male patients with myotonia congenita followed a standardised protocol with time scoring and rest on two occasions, with and without mexiletine. Time scoring of TUG and TST and self-assessments of stiffness were performed. A 14-day stiffness diary was used at home. Timed Up&Go and TST showed very good test–retest agreement (ICC=0.87–0.95) and significant to change (P