Long-term follow-up after repair of Ebstein's anomaly
- 作者：Meindert Palmen ; Peter L. de Jong ; Loes M.A. Klieverik ; Angelique C. Venema ; Folkert J. Meijboom ; Ad J.J.C. Bogers
- 关键词：Cardiac congenital ; Cyanotic ; Acyanotic ; Tricuspid valve
- 刊名：European Journal of Cardio-Thoracic Surgery
- 出版年：2008
- 期刊代码：89_10107940
- 类别：med
- 出版时间：July 2008
- 卷：34
- 期：1
- 页码：48-54
- 文件大小：172 K
摘要
Objective: We studied the long-term results of vertical plication repair of Ebstein's anomaly according to Carpentier. Methods: Between 1988 and 2007, 28 patients (mean age 28.8 ± 15.7 years, range 4–58 years) underwent vertical plication repair of Ebstein's anomaly. At operation the anomaly was classified according to Carpentier. In three patients (11%) a cavopulmonary shunt was added at the repair on the indication of impaired right ventricular function. Results: There was no operative mortality. Early mortality was 3.6%(one patient). Actuarial survival and actuarial freedom from reoperation at 19 years were 96%(95%CI; 96–97%) and 72%(95%CI; 53–92%), respectively. Six patients required reoperation, with a successful re-repair in three patients. Mean duration of follow-up was 10.7 ± 6.5 years. One year postoperatively, tricuspid incompetence had decreased significantly (p < 0.001), as had New York Heart Association (NYHA) functional class (p < 0.001). In addition, exercise tolerance had increased (70 ± 19%to 92 ± 9%of predicted values, p < 0.05). Both tricuspid function and NYHA functional class remained essentially unchanged at the end of follow-up, indicating durable haemodynamic and functional results. Conclusion: This study demonstrates favourable long-term results following vertical plication repair of Ebstein's anomaly with low mortality, acceptable morbidity and good haemodynamic and functional results.