• 作者：Ana Laura Calderó ; n-Garcidueñ ; as^a ; ^{acald911@hotmail.com} ; Tania Denisse Quintero-Valenzuela^a ; Santos Pavel Martí ; nez-Jaramillo^b ; Cé ; sar Ivan Peñ ; a-Ruelas^a ; Fortino Salazar-Salazar^b
• 关键词：Rabdomioma ; Fetal ; Intracraneal
• 刊名：Revista Espa帽ola de Patolog铆a
• 出版年：2011
• 期刊代码：pca318_16998855
• 类别：med
• 出版时间：October-December 2011
• 卷：44
• 期：4
• 页码：225-228
• 文件大小：269 K

Rhabdomyomas (RM) are benign, well circumscribed tumors consisting of striated muscle cells and are classified as cardiac or extracardiac, according to their location and histologically into adult or fetal types. Intracranial RM are extremely rare and are usually adult type tumors.

Clinical history

A 28 year old woman presented with a two month history of dizziness and progressive unilateral hearing loss. MRI showed a well-circumscribed, 6 脳 3 cm tumor in the right cerebello-pontine angle, which was T2 hyperintense with gadolinium reinforcement. The tumor compressed the anterior portion of the right cerebellar hemisphere and caused a notable displacement of the brain stem from right to left. A right retrosigmoid craniectomy was performed and 95%of the tumor was resected.

Conclusion

A case of extracardiac (intracranial) fetal type rhabdomyoma is reported for the first time in the cerebello-pontine angle of a female patient.