Sarcoidosis is a chronic multisystem disease of undetermined aetiology that involves mainly the lung. Affectation of the upper airways is rare, and it is very infrequent as the first manifestation. We report a case of laryngeal sarcoidosis in a 20-year-old woman. The diagnosis was based on clinical information, radiology, histopathology and laboratory tests. The treatment is systemic corticosteroids, as in the pulmonary sarcoidosis.