Airway ion transport impacts on disease presentation and severity in cystic fibrosis

详细信息	查看全文 | 推荐本文 |

• 作者：Teresinha Leal ; Isabelle Fajac ; Helen L. Wallace ; Patrick Lebecque ; Jean Lebacq ; Dominique Hubert ; Josette Dall'Ava ; Daniel Dusser ; Anusha P. Ganesan ; Christiane Knoop ; Jean Cumps ; Pierre Wallemacq ; K
• 关键词：Cystic fibrosis ; CFTR ; Membrane potentials ; Ion transport
• 刊名：Clinical Biochemistry
• 出版年：2008
• 期刊代码：55_00099120
• 类别：med
• 出版时间：July 2008
• 卷：41
• 期：10-11
• 页码：764-772
• 文件大小：378 K

摘要

Abnormal airway ion transport is a feature of cystic fibrosis. The aim of this study was to investigate whether distinct components of ion transport are associated with the clinical expression and severity of the disease.