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IgG4相关性硬化性胆管炎误诊为肝门部胆管癌1例报告
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  • 英文篇名:IgG4-related sclerosing cholangitis misdiagnosed as hilar cholangiocarcinoma:case report
  • 作者:易勇 ; 宋保东 ; 罗荣奎 ; 邱双健
  • 英文作者:YI Yong;SONG Bao-dong;LUO Rong-kui;QIU Shuang-jian;Department of Liver Surgery and Liver Transplantation,Zhongshan hospital,Fudan University;Department of Hepatobiliary Surgery,Changshu Second People's Hospital;Department of Pathology,Zhongshan hospital,Fudan University;
  • 关键词:IgG4相关性硬化性胆管炎 ; 肝门部胆管癌 ; 误诊
  • 英文关键词:IgG4-related sclerosing cholangitis;;hilar cholangiocarcinoma;;misdiagnosis
  • 中文刊名:LCYX
  • 英文刊名:Chinese Journal of Clinical Medicine
  • 机构:复旦大学附属中山医院肝肿瘤外科;常熟市第二人民医院肝胆外科;复旦大学附属中山医院病理科;
  • 出版日期:2019-02-25
  • 出版单位:中国临床医学
  • 年:2019
  • 期:v.26;No.137
  • 基金:国家自然科学基金(81302102)~~
  • 语种:中文;
  • 页:LCYX201901036
  • 页数:3
  • CN:01
  • ISSN:31-1794/R
  • 分类号:160-162
摘要
<正>1病例资料患者男性,75岁,2016年10月进食油腻食物后出现发热,体温最高39℃,无明显畏寒、寒战,伴右上腹持续性胀痛,皮肤、巩膜黄染,尿色加深。1.1外院诊治经过外院腹部超声示:慢性胆囊炎、胆囊结石、左肝内胆管多发结石伴扩张。患者于2016月11月7日行左半肝切除术+胆囊切除术+胆道镜取石术,术中见胆囊内数枚结石,胆总管下段少许泥沙样结石,左肝萎缩、表面可扪及结石,胆
        
引文
[1]NAKAZAWA T, NAITOH I, HAYASHI K, et al. Diagnosis of IgG4-related sclerosing cholangitis[J]. World J Gastroenteroournal, 2013,19(43):7661-7670.
    [2]MATSUSAKI S, KIKUYAMA M, KAWAKAMI H, et al. Clinical features and CT findings in the differential diagnosis of IgG4-related sclerosing cholangitis and cholangiocarcinoma[J]. Nihon Shokakibyo Gakkai Zasshi, 2013,110(4):615-621.
    [3]OKAZAKI K, UCHIDA K, KOYABU M, et al. IgG4 cholangiopathy: current concept, diagnosis, and pathogenesis[J]. J Hepatol, 2014, 61(3): 690-695.
    [4]马玲瑛, 马莉莉, 纪宗斐, 等. IgG4相关性疾病49例分析[J]. 中华风湿病学杂志, 2015,19(2):119-121,后插1.
    [5]RUNGSAKULKIJ N, SORNMAYURA P, TANNAPHAI P. Isolated IgG4-related sclerosing cholangitis misdiagnosed as malignancy in an area with endemic cholangiocarcinoma: a case report[J]. BMC Surg, 2017, 17(1):17.

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