摘要
报告3例Bart综合征。患儿为2女1男。出生后2例女童表现为单侧从膝部至足背皮肤缺损,男童表现为双侧从膝部至足背皮肤缺损。3例患儿均采用保守治疗,缺损皮肤恢复良好。随访至今,3例患儿皮肤缺损处表现为色素减退样瘢痕。该文对3例患者的临床资料进行总结并对相关文献进行了回顾。
Three cases of Bart syndrome are reported. The patients included two girls and one boy. Two girls presented with congenital localized absence of skin(CLAS) on the anterior and lateral surface of the right lower leg and the right dorsal foot at birth. The boy presented with bilateral and symmetrical congenital localized absence of skin on the anterior and lateral surface of both lower legs and dorsal feet at birth. All patients were given conservative treatments. The wounds completely healed with hypopigmented scars. Their clinical data were summarized, and related literatures were reviewed.
引文
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