不孕患者合并完全性子宫纵隔-双宫颈-阴道斜隔(有孔型)
摘要
苗勒管发育畸形的变化或组合可有多样,很难用某种综合征将其涵盖,按照宫体、宫颈和阴道分别描述并掌握处理原则更明晰。完全性子宫纵隔如合并不孕或反复流产,则具有明确的手术指征;双宫颈不需特殊处理;非梗阻性阴道纵隔如果影响性交才需要处理,而梗阻性阴道斜隔则必须切除。生殖道畸形的诊断看似复杂,但在熟悉胚胎发育学基础以及各种畸形分类系统的基础上是有规律可循的。此外,对于核磁影像的判读能力也是必要的,需要长期的积累和磨练。
引文
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[2]Shah DK,Laufer MR.Obstructed hemivagina and ipsilateral renal anomaly(OHVIRA)syndrome with a single uterus[J].Fertil Steril,2011,96:e39-e41.
[3]Haddad B,Barranger E,Paniel BJ.Blind hemivagina:longterm follow-up and reproductive performance in 42cases[J].Hum Reprod,1999,14:1962-1964.
[4]Fedele L,Motta F,Frontino G,et al.Double uterus with obstructed hemivagina and ipsilateral renal agenesis:pelvic anatomic variants in 87cases[J].Hum Reprod,2013,28:1580-1583.
[5]Kim MS,Nam SY,Lee G.Complete septate uterus,obstructed hemivagina,and ipsilateral adnexal and renal agenesis in pregnancy[J].Obstet Gynecol Sci,2014,57:310-313.
[6]邓姗,陈蓉,朱兰,等.子宫纵隔-双宫颈-阴道纵隔10例分析[J].中国实用妇科与产科杂志,2015,31:563-565.
[7]王姝,邓姗,朱兰,等.应用3D打印技术手术前诊断女性生殖道畸形附一例报告[J].中华妇产科杂志,2017,52:708-710.