摘要
目的探讨肺淋巴管肌瘤病(PLAM)的HRCT特征。方法对经病理证实的5例PLAM病例的HRCT特征表现进行回顾性分析。结果 PLAM的HRCT特征为两肺大小不等、弥漫及均匀分布的薄壁囊状影,肺纹理正常穿行于囊壁间,2例囊腔融合成肺大泡,1例伴乳糜性胸腔积液。结论育龄期女性患者出现两肺弥漫、均匀分布及大小不等的薄壁囊腔,结合临床表现可高度提示PLAM诊断。
引文
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