1例颅内窦组织细胞增生症伴巨淋巴结病的案例分析
摘要
<正>窦组织细胞增生症伴巨淋巴结(Rosai-Dorfman)病是一种良性组织细胞增生性疾病,因大多发生于淋巴结内,又称窦组织细胞增生伴巨淋巴结病,发病率低,且25%～43%发生于淋巴结外,如眼眶、皮肤、呼吸道、软组织、颅内、脊柱等。原发于中枢神经系统的Rosai-Dorfman病在该病中所占构成比低于4%,主要表现为幕上累及硬脑膜的实性肿块,术前多误诊为脑膜瘤,发生于脑实质内较为罕见,易误诊为淋巴瘤、脑转移瘤~([1])。其病因尚不明确,可能与某些病毒感染有关,如人疱疹病毒6、EB病毒、HIV等,但尚未证实~([2])。本研究对1例颅内Rosai-Dorfman病案例进行了分析,现报道如下。
引文
[1]HUANG B Y,ZONG M,ZONG W J,et al.Intracranial Rosai-Dorfman disease[J].J Clin Neurosci,2016,32:133-6.
[2]MANTILLA J G,GOLDBERG-STEIN S,WANG Y.Extranodal rosai-dorfman disease:clinicopathologic series of10patients with radiologic correlation and review of the literature[J].Am J Clin Pathol,2016,145(2):211-221.
[3]LUO Z,ZHANG Y,ZHAO P,et al.Characteristics of rosai-dorfman syndrome primarily involved in the central nervous system:a three-case report and review of literature[J].World Neurosurg,2016,97(7):58-63.
[4]柴学,张龙江,王娟,等.颅内原发性Rosai-Dorfman病:附3例报告并文献复习[J].医学影像学杂志,2013,21(12):1869-1872.
[5]丁鑫,焦彦超,吕彦,等.原发颅内孤立性Rosai-Dorfman病1例及文献复习[J].中国神经精神疾病杂志,2015,31(2):70.
[2]MANTILLA J G,GOLDBERG-STEIN S,WANG Y.Extranodal rosai-dorfman disease:clinicopathologic series of10patients with radiologic correlation and review of the literature[J].Am J Clin Pathol,2016,145(2):211-221.
[3]LUO Z,ZHANG Y,ZHAO P,et al.Characteristics of rosai-dorfman syndrome primarily involved in the central nervous system:a three-case report and review of literature[J].World Neurosurg,2016,97(7):58-63.
[4]柴学,张龙江,王娟,等.颅内原发性Rosai-Dorfman病:附3例报告并文献复习[J].医学影像学杂志,2013,21(12):1869-1872.
[5]丁鑫,焦彦超,吕彦,等.原发颅内孤立性Rosai-Dorfman病1例及文献复习[J].中国神经精神疾病杂志,2015,31(2):70.