Ⅲ型内耳不完全分隔耳蜗植入10例
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摘要
目的总结Ⅲ型内耳不完全分隔患者耳蜗植入的临床特点。方法分析10例Ⅲ型内耳不完全分隔患者的临床资料。结果 10例患儿产后检查均为重度感音神经性听力损失,颞骨磁共振及电子计算机断层扫描成像诊断单纯IP-Ⅲ畸形7例、IP-Ⅲ合并大前庭水管综合征1例;IP-Ⅲ合并IP-Ⅱ型耳蜗畸形2例。10例患者均成功植入人工耳蜗,术中井喷9例,术中CT示电极位置均正常,术后超声示皮下均无大量渗液;1～4周内开机调机正常,12个月后听力测试稳定,听阈测试平均为(39.11±6.61)dB HL,语言识别率平均为45%,扬扬格词表平均为61%。结论Ⅲ型内耳不完全分隔患儿植入耳蜗有井喷风险,应做好预防及补救措施,植入耳蜗后随访患者听力恢复效果佳。
引文
[1]龙墨.从美国教育听力学到我国听障儿童的听能管理[J].中国听力语言康复科学杂志,2012,10(2):142-144.
[2]邓忠,赖若沙,胡鹏.极重度感音神经性聋儿童的病因学分析[J].中国现代医学杂志,2011,21(33):4207-4211.
[3]SENNARO?LU L,DEMIR B M.Classification and current management of inner ear malformations[J].Balkan Medical Journal,2017,34(5):397-411.
[4]NANCE W E,SETLEFF R C,MCLEOD A,et al.X-linked mixed deafness with congenital fixation of the stapedial footplate and perilymphatic gusher[J].Birth defects original article series,1971,7(4):64-69.
[5]SENNAROGLU L.Histopathology of inner ear malformations:Do we have enough evidence to explain pathophysiology[J].Cochlear Implants International,2015,17(1):3-20.
[6]INCESULU A,ADAPINAR B,KECIK C.Cochlear implantation in cases with incomplete partition typeⅢ(X-linked anomaly)[J].European Archives of Oto-Rhino-Laryngology,2008,265(11):1425-1430.
[7]PHELPS P D,REARDON W,PEMBREY M,et al.X-linked deafness,stapes gushers and a distinctive defect of the inner ear[J].Neuroradiology,1991,33(4):326-330.
[8]KANNO A,MUTAI H,NAMBA K,et al.Frequency and specific characteristics of the incomplete partition type III anomaly in children[J].Laryngoscope,2016,127(7):1663.
[9]TALBOT J M,WILSON D F.Computed tomographic diagnosis of X-linked congenital mixed deafness,fixation of the stapedial footplate,and perilymphatic gusher[J].American Journal of Otology,1994,15(2):177.
[10]MELO A S,MARTINS J,SILVA J,et al.Cochlear implantation in children with anomalous cochleovestibular anatomy[J].Laryngoscope,2005,115(S):1-26.
[11]王超,王丽娜,肖玉丽,等.Nucleus人工耳蜗电极阻抗测试的研究[J].中国现代医学杂志,2006,16(1):92-94.
[12]陈杰,杨烨,林川耀,等.70例大前庭水管综合征患者的人工耳蜗植入效果分析[J].中国现代医学杂志,2015,25(14):73-75.
[13]李万鑫,刘军,武文明,等.人工耳蜗植入术中脑脊液井喷的原因分析及处理[J].中华耳科学杂志,2017,15(4):436-440.
[2]邓忠,赖若沙,胡鹏.极重度感音神经性聋儿童的病因学分析[J].中国现代医学杂志,2011,21(33):4207-4211.
[3]SENNARO?LU L,DEMIR B M.Classification and current management of inner ear malformations[J].Balkan Medical Journal,2017,34(5):397-411.
[4]NANCE W E,SETLEFF R C,MCLEOD A,et al.X-linked mixed deafness with congenital fixation of the stapedial footplate and perilymphatic gusher[J].Birth defects original article series,1971,7(4):64-69.
[5]SENNAROGLU L.Histopathology of inner ear malformations:Do we have enough evidence to explain pathophysiology[J].Cochlear Implants International,2015,17(1):3-20.
[6]INCESULU A,ADAPINAR B,KECIK C.Cochlear implantation in cases with incomplete partition typeⅢ(X-linked anomaly)[J].European Archives of Oto-Rhino-Laryngology,2008,265(11):1425-1430.
[7]PHELPS P D,REARDON W,PEMBREY M,et al.X-linked deafness,stapes gushers and a distinctive defect of the inner ear[J].Neuroradiology,1991,33(4):326-330.
[8]KANNO A,MUTAI H,NAMBA K,et al.Frequency and specific characteristics of the incomplete partition type III anomaly in children[J].Laryngoscope,2016,127(7):1663.
[9]TALBOT J M,WILSON D F.Computed tomographic diagnosis of X-linked congenital mixed deafness,fixation of the stapedial footplate,and perilymphatic gusher[J].American Journal of Otology,1994,15(2):177.
[10]MELO A S,MARTINS J,SILVA J,et al.Cochlear implantation in children with anomalous cochleovestibular anatomy[J].Laryngoscope,2005,115(S):1-26.
[11]王超,王丽娜,肖玉丽,等.Nucleus人工耳蜗电极阻抗测试的研究[J].中国现代医学杂志,2006,16(1):92-94.
[12]陈杰,杨烨,林川耀,等.70例大前庭水管综合征患者的人工耳蜗植入效果分析[J].中国现代医学杂志,2015,25(14):73-75.
[13]李万鑫,刘军,武文明,等.人工耳蜗植入术中脑脊液井喷的原因分析及处理[J].中华耳科学杂志,2017,15(4):436-440.