血糖升高为首发症状的IgG4相关性疾病一例
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摘要
<正>IgG4相关疾病(IgG4-RD)是一种新近认识的纤维炎症性疾病,可同时或逐渐累及多个器官,受累器官主要表现为弥漫性或局灶性肿大、肿块形成、结节状或增厚病灶,组织病理学表现为广泛的IgG4阳性浆细胞浸润、纤维化~([1])。该病几乎所有器官均可能受累,最常见的受累器官是胰腺、肾脏、眶周组织、唾液腺和腹膜后组织。该病致病机制尚不确切,目前类固醇激素治疗效果良好,但其远期疗效尚不清楚。IgG4-RD早期表现常不典型,可出现类似肿瘤、感染或免疫相关
        
引文
[1]OKAZAKI K,UCHIDA K.Current perspectives on autoimmune pancreatitis and IgG4-related disease[J].Proc Jpn Acad Ser B Phys Biol Sci,2018,94(10):412-427.
    [2]GOODCHILD G,STEPHEN PP,WEBSTER G.Immunoglobulin G4-related sclerosing cholangitis[J].Korean J Intern Med,2018,33(5):841-850.
    [3]DETLEFSEN S,KL?PPEL G.Histopathology of IgG4-related disease[J].Z Rheumatol,2016,75(7):666-674.
    [4]OPRIT?R,OPRIT?B,BERCEANU D,et al.Overview of IgG4-related disease[J].J Med Life,2017,10(4):203-207.
    [5]SMERLA RG,RONTOGIANNI D,FRAGOULIS GE.Ocular manifestations of IgG4-related disease in children.More common than anticipated?Review of the literature and case report[J].Clin Rheumatol,2018,37(6):1721-1727.
    [6]EL EUCH M,HDDAD S,MAHFOUDHI M,et al.A Case of type 1autoimmune pancreatitis(AIP),a form of IgG4-related disease(IgG4-RD)[J].Am J Case Rep,2017,18(7):822-825.
    [7]INOUE D,YOSHIDA K,YONEDA N,et al.IgG4-related disease:dataset of 235 consecutive patients[J].Medicine(Baltimore),2015,94(15):e680.
    [8]OBIORAH IE,VELASQUEZ AH,?ZDEMIRLI M.The clinicopathologic spectrum of IgG4-related disease[J].Balkan Med J,2018,35(4):292-300.
    [9]AL-MUJAINI A,AL-KHABORI M,SHENOY K,et al.Immunoglobulin G4-related disease:an update[J].Oman Med J,2018,33(2):97-103.
    [10]Salvadori M,Tsalouchos A.Immunoglobulin G4-related kidney diseases:An updated review[J].World J Nephrol,2018,7(1):29-40.

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