摘要
青斑样血管病是一种非炎性、真皮内血管阻塞性皮肤病,以双下肢远端反复出现疼痛性溃疡、网状青斑以及瓷白色萎缩性瘢痕为主要临床表现。青瘢样血管病的病因不明,可能的致病因素有机体高凝状态、纤维蛋白溶解障碍和(或)与免疫系统疾病相关。阎小萍教授认为,本病主要病机因先天不足,肺脾肾三经虚弱,卫外不固,风寒湿邪乘虚而入,阻于脉络,久瘀化热,蕴而成毒,内舍于脏腑,脏腑功能失调,以虚实夹杂为多,治宜扶正祛邪、标本兼治。从改善疾病本质入手,经过临床实践,取得较好疗效。
引文
[1]FELAKER M,HINES EA,KIERLAND RR.Livedo reticularis with summer ulcerations[J].AMA Arch Dermatol,1955,72(1):31-42.
[2]CRIADO PR,RIVITTI EA,SOTTO MN,et al.Livedoid vasculopathy as a coagulation disorder[J].Autoimmun Rev,2011,10(6):353-360.
[3]CRIADO PR,RIVITTI EA,SOTTO MN,et al.Livedoid vasculopathy:an intringuing cutaneous disease[J].An Bras Dermatol,2011,86(5):961-977.
[4]VASCONCELOS R,CRIADO PR,BELDA W JR.Libedoid vasculopathy secondary to high levels of lipoprotein(a)[J].Br J Dermatol,2011,164(5):1111-1113.
[5]冯素英,林麟,靳培英.皮肤假性血管炎[J].临床皮肤科杂志,2011,40(2):118-121.
[6]HAIRSTON BR,DAVIS MD,GIBSON LE,et al.Treatment of livedoid vasculopathy with low-molecular-weight hepatin:report of 2 cases[J].Arch Dermatol,2003,139(8):987-990.
[7]孙昂远,刘越阳,李铁男,等.雷公藤多甙联合低分子肝素/氯吡格雷治疗青斑样血管病10例[J].中国皮肤性病学杂志,2016,30(6):591-592.
[8]FRITSCH P,ZELGER B.Libedo vasculitis[J].Hautarzt,1995,46(3):215-224.
[9]李洪利,朱明兴,宋彦奇,等.白色萎缩从脉痹治验个案报道[J].山东中医杂志,2017,36(7):609-610,613.
[10]阎小萍,张煜,翁习生.常见风湿病及相关骨科疾病中西医结合诊治[M].北京:人民卫生出版社,2015:178-181.
[11]胡凤侠,丁媛,康晓静.青斑样血管炎18例临床分析[J].中国皮肤性病学杂志,2017,31(1):36-38
[12]闫雨荷,崔炳南,吴小红.青斑样血管病的诊疗进展[J].中国麻风皮肤病杂志,2017,33(4):254-256