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在“Elsevier电子期刊”中，命中：352条，耗时：0.0249874 秒

在所有数据库中总计命中：501条

1.Ginger extract increases muscle mitochondrial biogenesis and serum HDL-cholesterol level in high-fat diet-fed rats

作者：Soojung Oh^a ; ¹ ; Mak-Soon Lee^a ; ¹ ; Sunyoon Jung^a ; ¹ ; Seunghae Kim^a ; Hyeyoung Park^a ; Seonyoung Park^a ; Seog-Young Kim^a ; Chong-Tai Kim^b ; Young-Hee Jo^b ; In-Hwan Kim^c ; Yangha Kim^a ; ^{yhmoon@ewha.ac.kr}

关键词：ABCA1 ; ATP-binding cassette transporter A1 ; ApoA-1 ; apolipoprotein A-1 ; CYP7A1 ; 7 alpha-hydroxylase ; GEH ; high-fat diet containing 0.5% ginger extract ; GEL ; high-fat diet containing 0.25% ginger extract ; HDL-C ; high-density lipoprotein-cholesterol ; HF ; high-fat diet ; LCAT ; lecithin-cholesterol acyltransferase ; LDL-C ; low-density lipoprotein-cholesterol ; mtDNA ; mitochondrial DNA ; NRF ; nuclear respiratory factor ; PGC-1α ; peroxisome proliferator-activated receptor γ coactivator-1α ; PPAR ; peroxisome

刊名：Journal of Functional Foods

出版年：2017

2.Adaptive responses of neuronal mitochondria to bioenergetic challenges: Roles in neuroplasticity and disease resistance

作者：Sophia M. Raefsky^a ; Mark P. Mattson^a ; ^b ; ^{mark.mattson@nih.gov}

关键词：3-hydroxybutyrate ; Aerobic exercise ; Autophagy ; CREB ; Hormesis ; Intermittent fasting ; Mitochondrial biogenesis ; PGC-1α

刊名：Free Radical Biology and Medicine

出版年：2017

3.“Role of peroxisomes in human lipid metabolism and its importance for neurological development”

作者：Ronald J.A. Wanders^a ; ; Bwee Tien Poll-The^b ; ^{r.j.wanders@amc.uva.nl}

关键词：Peroxisomes ; Peroxisomal disorders ; Lipidomics ; Lipids ; Fatty acids ; Mitochondria

刊名：Neuroscience Letters

出版年：2017

4.Absence of biochemical evidence at an early age delays diagnosis in a patient with a clinically severe peroxisomal biogenesis disorder

作者：Natalia Lü ; sebrink^a ; ^{Natalia.Luesebrink@kgu.de" class="auth_mail" title="E-mail the corresponding author} ; Luciana Porto^b ; Hans R. Waterham^c ; Sacha Ferdinandusse^c ; Hendrik Rosewich^d ; Gerd Kurlemann^e ; Matthias Kieslich^a

关键词：Peroxisomal biogenesis disorder ; Zellweger spectrum disorder ; PEX6 ; Polimicrogyria ; VLCFA

刊名：European Journal of Paediatric Neurology

出版年：2016

5.Peroxisome biogenesis disorders in the Zellweger spectrum: An overview of current diagnosis, clinical manifestations, and treatment guidelines

关键词：AAV ; adeno-associated virus ; AED ; anti-epileptic drug(s) ; DHA ; docosahexaenoic acid ; DHCA ; dihydroxycholestanoic acid ; ERG ; electroretinogram ; G-tube ; gastrostomy tube ; IRD ; infantile Refsum disease ; LC-MS/MS ; liquid chromatography/tandem mass spectrometry ; NALD ; neonatal adrenoleukodystrophy ; OCT ; optical coherence tomography ; PBD ; peroxisome biogenesis disorder ; PBD-ZSD ; peroxisome biogenesis disorder-Zellweger spectrum disorder ; THCA ; trihydroxycholestanoic acid ; VLCFA ; very long chain fatty

刊名：Molecular Genetics and Metabolism

出版年：2016

6.Hepatic dysfunction in peroxisomal disorders

作者：Myriam Baes^a ; ^{myriam.baes@pharm.kuleuven.be" class="auth_mail" title="E-mail the corresponding author} ; Paul P. Van Veldhoven^b ; ^{paul.vanveldhoven@med.kuleuven.be" class="auth_mail" title="E-mail the corresponding author}

关键词：ABC ; ATP-binding cassette ; ACAA1 ; acetyl-CoA acyltransferase ; ACOX ; acyl-CoA oxidase ; BAAT ; bile acid CoA-amino acid N-acyl transferase ; C24-bile acid ; cholanoic acid ; C27-bile acid ; cholestanoic acid ; CDCA ; chenodeoxycholic acid ; Cn-DCA ; straight chain dicarboxylic acid with n C atoms ; DCA ; dicarboxylic acid ; DHA ; docosahexaenoic acid ; DHCA ; dihydroxycholestanoic acid ; HAO ; 2-hydroxy acid oxidase ; ER ; endoplasmic reticulum ; MFP ; multifunctional protein ; PBD ; peroxisome biogenesis disorder ; PMP

刊名：Biochimica et Biophysica Acta (BBA)-Molecular Cell Research

出版年：2016

7.A new multiplex method for the diagnosis of peroxisomal disorders allowing simultaneous determination of plasma very-long-chain fatty acids, phytanic, pristanic, docosahexaenoic and bile acids by high-performance liquid chromatography-atmospheric pressure chemical ionization-tandem mass spectrometry

作者：Michela Semeraro^a ; ¹ ; ^{michela.semeraro@opbg.net" class="auth_mail" title="E-mail the corresponding author} ; Cristiano Rizzo^a ; ¹ ; Sara Boenzi^a ; Marco Cappa^b ; Enrico Bertini^c ; Giacomo Antonetti^a ; Carlo Dionisi-Vici^a

关键词：PDs ; peroxisomal disorders ; LC-MS/MS ; liquid chromatography-tandem mass spectrometry ; CV ; coefficient of variation ; VLCFAs ; very-long-chain fatty acids ; Pri ; pristanic acid ; PUFAs ; polyunsaturated fatty acids ; DHA ; docosahexaenoic acid ; Phy ; phytanic acid ; PBDs ; peroxisomal biogenesis disorders ; GC&ndash ; MS ; gas chromatography&ndash ; mass spectrometry ; ESI-MS/MS ; electrospray ionization tandem mass spectrometry ; UPLC ; ultra-performance liquid chromatography ; DAABD-AE ; 4-[2-(N ; N-dimethylamino) eth

刊名：Clinica Chimica Acta

出版年：2016

8.Peroxisome biogenesis in mammalian cells: The impact of genes and environment

作者：Rebecca L. Farr^a ; ^b ; Celien Lismont^a ; Stanley R. Terlecky^b ; Marc Fransen^a ; ^{marc.fransen@med.kuleuven.be" class="auth_mail" title="E-mail the corresponding author}

刊名：Biochimica et Biophysica Acta (BBA)-Molecular Cell Research

出版年：2016

9.Low bone mineral density is a common feature of Zellweger spectrum disorders

作者：Eric T. Rush^a ; ^b ; ^c ; ^{erush@unmc.edu" class="auth_mail" title="E-mail the corresponding author} ; Jennifer L. Goodwin^a ; Nancy E. Braverman^d ; William B. Rizzo^a ; ^c

关键词：Peroxisomal biogenesis disorder ; Zellweger spectrum disorder ; Bone mineral density ; Bone densitometry ; PPAR-gamma ; Pathologic fracture ; Bisphosphonate

刊名：Molecular Genetics and Metabolism

出版年：2016

10.Human disorders of peroxisome metabolism and biogenesis

作者：Hans R. Waterham ; ^{h.r.waterham@amc.uva.nl" class="auth_mail" title="E-mail the corresponding author} ; Sacha Ferdinandusse ; Ronald J.A. Wanders

关键词：ACAA1 ; 3-ketoacyl-CoA thiolase ; ACOX1 ; Acyl-CoA oxidase 1 ; ACOX2 ; acyl-CoA oxidase 2 ; ABCD1 ; ABC transporter D1 ; ABCD2 ; ABC transporter D2 ; ABCD3 ; ABC transporter D3 ; AGPS ; alkyl-dihydroxyacetonephosphate synthase ; AGT ; alanine-glyoxylate aminotransferase ; AMACR ; 2-methylacyl-CoA racemace ; BAAT ; Bile acid&ndash ; CoA ; amino acid N-acyltransferase ; brAcyl ; branched-acyl ; CA ; cholic acid ; CAT ; catalase ; CDCA ; chenodeoxycholic acid ; CoA ; coenzyme A ; DBP ; D-bifunctional protein ; DCA ; dicarboxylic acids

刊名：Biochimica et Biophysica Acta (BBA)-Molecular Cell Research

出版年：2016

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